Doege-Potter Syndrome:  A Presumptive Case of Metastatic Hemangiopericytoma  with Persistent Hypoglycemia in a 27-Year-Old Male

Von Lovel Zarra; Kenny Jun Demegillo; May Uyking-Naranjo; Ahmad Domado

doi:10.15605/jafes.036.01.16

Authors

Von Lovel Zarra Southern Philippines Medical Center, Davao City, Philippines https://orcid.org/0000-0002-4551-9434
Kenny Jun Demegillo Southern Philippines Medical Center, Davao City, Philippines
May Uyking-Naranjo Southern Philippines Medical Center, Davao City, Philippines
Ahmad Domado Southern Philippines Medical Center, Davao City, Philippines

DOI:

https://doi.org/10.15605/jafes.036.01.16

Keywords:

Doege-Potter syndrome, hemangioperictyoma, hypoglycemia

Abstract

Doege-Potter syndrome (DPS) is a rare paraneoplastic condition characterized by hypoinsulinemic hypoglycemia from a solitary fibrous tumor. The underlying mechanism is the secretion of a prohormone form of insulin-like growth factor II (IGF-II) by the tumor, which causes decreased release of glucose into the circulation. We report the case of a 27-year-old Filipino male with presumptive DPS from a recurrent right temporo-zygomatic hemangiopericytoma (HPC). The complexity of DPS requires a multidisciplinary approach. Early screening for metastases from HPC may prevent the undesirable sequelae of the disease process.

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Author Biographies

Von Lovel Zarra, Southern Philippines Medical Center, Davao City, Philippines

Medical Officer III, Department of Internal Medicine

Kenny Jun Demegillo, Southern Philippines Medical Center, Davao City, Philippines

Medical Specialist, Department of Endocrinology

May Uyking-Naranjo, Southern Philippines Medical Center, Davao City, Philippines

Medical Specialist, Section of Endocrinology, Department of Internal Medicine

Ahmad Domado, Southern Philippines Medical Center, Davao City, Philippines

Department of Internal Medicine

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